Possible ocular involvement in pulmonary alveolar proteinosis.
نویسندگان
چکیده
Pulmonary alveolar proteinosis (PAP) is a rare lung disease characterised by lipoproteinaceous material accumulation in the alveoli. In the most frequent form of the disease (acquired PAP), a neutralising auto-antibody against granulocytemacrophage colony-stimulating factor (GM-CSF) causes defects in the functioning of alveolar macrophages, including impairment of the catabolism of surfactant lipids and proteins [1].
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ورودعنوان ژورنال:
- The European respiratory journal
دوره 28 2 شماره
صفحات -
تاریخ انتشار 2006